Materials and Methods All chemicals except those stated below were obtained from Merck. HPLC-grade dimethyl sulfoxide and HCl were obtained from Aldrich.
Cystine deficiency is not clinically significant since the absorption of cystine is unaffected. The clinical picture of cystinuria therefore remains a problem of stone disease.
Since, even in proved cases of cystinuria, the typical hexagonal cystine crystals are not always present in the urine, especially when dilute or fresh specimens are examined.
SULFUR IN PROTEINS. III. DERIVATIVES OF I- AND i-CYSTINE.* BY ROSSAIKENGORTNER AND WALTERF.HOFFMAN. (From the Division of Agricultural Biochemistry, University of Minnesota,
THE Jonmar. OF BIOLOQIC~L CHEMISTRY Vol. 236, No. 5, May 1961 Printed in U.S.A. The Biosynthesis of Cystine in Human Cell Cultures
565 Cystine Calculi are Radiopaque Robert C. Brow& Stefan A. Loening2 JamesC. Ehrhardt1 Charles E. Hawtrey2 Received February 7,1980; accepted after revision May 12,1980.
Toward a Better Breed—The Deerhound Cystinuria Study Last year I wrote about a potentially life-threatening inherited disease called cystinuria, in which the amino acid cystine gets into the urine where it doesn't belong.
The rule of thumb is to drink one litre of liquids for every millimole of cystine to keep the average concentration below 1 millimole. If the 24 hour cystine were 1500 mg (about 6 millimoles), one would need at least 6 liters of water.
The Importance of Accurate Cystine Level Testing Neil Dalton of The Evelina Childrens Hospital, London. January 2009 The importance of measuring white cell (leucocyte) cystine The importance of white cell cystine measurements in the diagnosis and clinical management of patients with cystinosis ...
NEPHROLOGY 2007; 12 , S4-S10 doi:10.1111/j.1440-1797.2006.00722.x © 2007 The Author Journal compilation © 2007 Asian Pacific Society of Nephrology Blackwell Publishing AsiaMelbourne, AustraliaNEPNephrology1320-5358© 2006 The Authors; Journal compilation © 2006 Asian Pacific Society of ...